Treatment of Cystic Fibrosis and Other Rare Lung Diseases

Part I. Etiopathology and Genetics of Rare Lung Diseases

1. An Introduction to Clinical Aspects of Cystic Fibrosis
Nauman Chaudary, Michael S. Schechter

2. Diffuse Panbronchiolitis
Naoto Keicho, Minako Hijikata

3. Idiopathic Pulmonary Fibrosis
Chiko Shimbori, Pierre-Simon Bellaye, Philipp Kolb, Martin Kolb

4. Pulmonary Alveolar Proteinosis: A Historic Perspective
Koh Nakata, Ryushi Tazawa

5. Lymphangioleiomyomatosis
Kuniaki Seyama

Part II. Treatment of Cystic Fibrosis

6. CFTR Modulator Therapies in Cystic Fibrosis
David R. Spielberg, John P. Clancy, Christopher Siracusa

7. Drug Therapies that Augment Airway Surface Liquid
Evangelia Daviskas, Sheila Sivam, Mark R. Elkins, Tiffany J. Dwyer, Ruth Dentice, Peter T. Bye

8. Anti-Inflammatory Therapies for Cystic Fibrosis
Elliott C. Dasenbrook, James F. Chmiel

9. Anti-Infective Therapies in Cystic Fibrosis
Patrick A. Flume, Donald R. VanDevanter

Part III. Treatment of Other Rare Lung Diseases

10. Diffuse Panbronchiolitis: Long-Term Low-Dose Macrolide Therapy
Mutsuo Yamaya, Arata Azuma, Shoji Kudoh

11. Idiopathic Pulmonary Fibrosis
Paolo Spagnolo

12. Treatment of Pulmonary Alveolar Proteinosis
Muhammad Muhye-ud-din Sheikh, Bruce C. Trapnell

13. Treatment of Lymphangioleiomyomatosis (LAM)
Mariam Anis, Francis X. McCormack

Nyckelord: Biomedicine, Pharmacology/Toxicology, Pneumology/Respiratory System, Internal Medicine, Immunology